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Date Published: 16/05/2025
Abstract Views: 57
Views pdf: 30
DOI: https://doi.org/10.55046/vjrnm.58.1181.2025
Issue
No. 58 (2025)
Section
Medical Forum
How to Cite
Sử, T. M. H., Le, T. D., Dong, V. H., & Nguyen, S. L. (2025). NEUROCUTANEOUS MELANOSIS: a case of Viet Duc Hospital. Vietnamese Journal of Radiology and Nuclear Medicine, 58, 74-79. https://doi.org/10.55046/vjrnm.58.1181.2025

NEUROCUTANEOUS MELANOSIS: a case of Viet Duc Hospital

Thị Mỹ Hà Sử1, , Le Thanh Dung2, Dong Van He3, Nguyen Sy Lanh4
1 Bệnh viện Việt Đức
2 Department of Diagnostic Imaging, Viet Duc Friendship Hospital
3 Neurosurgery Center, Viet Duc Friendship Hospital
4 Department of Pathology, Viet Duc Friendship Hospital

Main Article Content

Abstract

Neurocutaneous melanosis is a rare congenital disorder which presents with congenital
cutaneous nevi and involvement of the central nervous system. Here we present a rare case of a
27-year-old mem who had central nervous system melanosis and giant congenital melanocytic
nevi. A brain computed tomography (CT) scan revealed a high-density lesion in the left temporal
lobe, suggesting hemorrhage, no vascular abnormality was seen on CT angiography (CTA).
Magnetic resonance imaging (MRI) showed occupying lesions in the left temporal lobe,
leptomeningeal with high signals on T1WI and isosignals on T2WI, and with significant
enhancement after administration of gadolinium. The confirmed diagnosis is established by
surgical tissue and leptomeningeal biospy.
Keywords: Neurocutaneous melanosis, Leptomeningeal melanoma, Primary melanoma

Keywords

Neurocutaneous melanosis, Leptomeningeal melanoma, Primary melanoma

Article Details

References

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