Article Sidebar

pdf
Date Published: 16/05/2025
Abstract Views: 171
Views pdf: 64
DOI: https://doi.org/10.55046/vjrnm.58.1245.2025
Issue
No. 58 (2025)
Section
Medical Forum
How to Cite
Ngô, V. H., Trần, P. N., & Chu, N. H. (2025). CONGENITAL PORTOSYSTEMIC SHUNT IN CHILDREN: CASE REPORTS. Vietnamese Journal of Radiology and Nuclear Medicine, 58, 80-86. https://doi.org/10.55046/vjrnm.58.1245.2025

CONGENITAL PORTOSYSTEMIC SHUNT IN CHILDREN: CASE REPORTS

Văn Hùng Ngô1, , Trần Phan Ninh, Chu Nguyên Hải
1 Bệnh viện Nhi Trung ương

Main Article Content

Abstract

Congenital portosystemic shunt is a rare vascular anomaly characterized by an abnormal connection between the portal vein and the inferior vena cava, resulting in partial or complete diversion of blood flow from the portal vein to the systemic circulation without passing through the liver. Portosystemic shunts can be classified into various types and are often associated with cardiovascular anomalies or other congenital defects. Major complications include liver disease, hepatic tumors, portopulmonary hypertension, and pulmonary arteriovenous shunts. Imaging plays a crucial role in diagnosing congenital portosystemic shunts and associated abnormalities. Computed tomography is considered the first choice for diagnosing shunts, determining the type of shunt, and visualizing blood vessels and small liver lesions. Treatment indications depend on the type of shunt and clinical progression, and may involve shunt occlusion through surgery or endovascular intervention. In this report, we present three cases of congenital portosystemic shunt that were definitively diagnosed by computed tomography, including a type 2 side-to-side congenital portosystemic shunt according to Bicêtre classification treated successfully with endovascular intervention, a type 4 congenital portosystemic shunt, and a type 2 end-to-side shunt according to Bicêtre classification treated successfully with open surgical banding of the shunt.


 


Keywords

Congenital portosystemic shunt, Abernethy malformation, Bicêtre classification, computed tomography

Article Details

Author Biographies

Trần Phan Ninh

 

 

TRANSLATE with x English Arabic Hebrew Polish Bulgarian Hindi Portuguese Catalan Hmong Daw Romanian Chinese Simplified Hungarian Russian Chinese Traditional Indonesian Slovak Czech Italian Slovenian Danish Japanese Spanish Dutch Klingon Swedish English Korean Thai Estonian Latvian Turkish Finnish Lithuanian Ukrainian French Malay Urdu German Maltese Vietnamese Greek Norwegian Welsh Haitian Creole Persian     TRANSLATE with COPY THE URL BELOW Back EMBED THE SNIPPET BELOW IN YOUR SITE Enable collaborative features and customize widget: Bing Webmaster Portal Back

Chu Nguyên Hải

 

 

TRANSLATE with x English Arabic Hebrew Polish Bulgarian Hindi Portuguese Catalan Hmong Daw Romanian Chinese Simplified Hungarian Russian Chinese Traditional Indonesian Slovak Czech Italian Slovenian Danish Japanese Spanish Dutch Klingon Swedish English Korean Thai Estonian Latvian Turkish Finnish Lithuanian Ukrainian French Malay Urdu German Maltese Vietnamese Greek Norwegian Welsh Haitian Creole Persian     TRANSLATE with COPY THE URL BELOW Back EMBED THE SNIPPET BELOW IN YOUR SITE Enable collaborative features and customize widget: Bing Webmaster Portal Back

References

1. Xu S, Zhang P, Hu L, Zhou W, Cheng G. Case Report: Clinical Features of Congenital Portosystemic Shunts in the Neonatal Period. Front Pediatr. 2021;9:778791.
2. Păcurar D, Dijmărescu I, Dijmărescu AD, Romaşcanu M, Becheanu CA. A case report on an incidental discovery of congenital portosystemic shunt. Medicine. 2019;98(31):e16679.
3. Timpanaro T, Passanisi S, Sauna A, et al. Congenital Portosystemic Shunt: Our Experience. Case Reports in Pediatrics. 2015;2015:1-5.
4. Guo C, Zhong YM, Wang Q, et al. Diagnostic accuracy of multi-slice computed tomography in children with Abernethy malformation. BMC Med Imaging. 2019;19(1):97.
5. The International Registry of Congenital Portosystemic Shunt members, Franchi-Abella S, Gonzales E, et al. Congenital portosystemic shunts: diagnosis and treatment. Abdom Radiol. 2018;43(8):2023-2036.
6. Rajeswaran S, Johnston A, Green J, et al. Abernethy Malformations: Evaluation and Management of Congenital Portosystemic Shunts. Journal of Vascular and Interventional Radiology. 2020;31(5):788-794.
7. Papamichail M, Pizanias M, Heaton N. Congenital portosystemic venous shunt. Eur J Pediatr. 2018;177(3):285-294.
8. Tamiru R, Hailemariam T, Wakjira E, Hailu SS. Congenital extrahepatic portosystemic shunt masquerading as chronic portal vein thrombosis: A case report. International Journal of Surgery Case Reports. 2023;109:108553