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PRIMARY HEPATIC ANGIOSARCOMA: A CASE REPORT
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Abstract
SUMMARY
We report a case who was diagnosed with primary hepatic angiosarcoma (PHA). A 62-year-old man presented with right upper quadrant abdominal pain, weight loss and hepatomegaly. He had no relevant medical history or exposure history. On laboratory evaluation, the patient had an elevation of white blood cell count, AST, ALT and anemia, the levels of serum carcinoembryonic antigen, carbohydrate antigen (CA)‑199, α‑fetoprotein and PIVKA-II were normal. Abdominal computed tomography and magnetic resonance imaging revealed a large lession in the right lobe of the liver and a small lesion in the left lobe of the liver suggesting PHA. The patient underwent liver biopsy and histopathological examination confirmed PHA.
PHA is a rare disease, usually occurs in the sixth decade of life and males are more frequently affected than females. In most cases, the cause is unknown. Clinical symptoms and laboratory evaluation of PHA are nonspecific. Imaging findings help detect liver tumors and suggest a diagnosis of PHA, in which CTA is the modality of choice. Liver biopsy and histopathology confirmed the presence of PHA.
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Keywords
angiosarcoma, primary hepatic angiosarcoma
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