CT scanner and MRI imagingof cochlear nerve deficiency in 22 patients with bilateral congenital sensorineural hearing loss

Le Duy Chung1, Cao Minh Thanh2, Pham Hong Duc3,
1 Department of Diagnostic Imaging, Hanoi Medical University Hospital
2 Department of Neurology, Hanoi Medical University Hospital
3 Diagnostic Imaging Department of Saint Paul Hospital

Main Article Content

Abstract

SUMMARY


Objective: To describe CT scanner and MRI imagingof cochlear nerve deficiency (CND) and cochleovestibular nerve abnormality in association with cochlear aperture, internal auditory canal (IAC) and labyrinthine malformations.
Material and Methods: 22 patients with CNDin 43 ears. Aplasia
or hypoplasia of the cochlear branch was evaluated on high resolution
3D gradient-echo MRI. Cochlear aperture, IAC and bony labyrinthine malformations was evaluated on high resolutionCT scanner.
Results: 22 patients with CNDin 43 ears. Cochlear nerve aplasia in 20 ears (46,5%), cochlear nerve hypoplasia in 2 ears (4,7%), presence of vestibulocochlear nerve with no cochlear branch in 21 ears (48,8%). Labyrinthine malformation in 25 ears (58,1%).The mean IAC diameter 3,03 ± 1,03mm.Cochlear aperture stenosis and atresia 76,7%.
Conclusion:CND frequently associated with labyrinthine malformations, cochlear aperture stenosis or atresia and IAC stenosis.

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References

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